The practice of pediatrics . fat which are most marked in thepseudohypertrophic form are secondary to the atrophy of the musclefibres. The giant muscle fibres are probably an attempt at compensa-tory hypertrophy. Symptomatology. (a) Landouzy-Dejerine Type.—This type usuallydevelops in early childhood, but I have seen two cases develop in adultlife. The peculiar features are the early atrophy affecting the musclesof the face beginning in the orbicularis oris and extending to the levatormenti, the risorii, and later to the other muscles of the face. The lips ABIOTROPHIC DISEASES 921 become weak
The practice of pediatrics . fat which are most marked in thepseudohypertrophic form are secondary to the atrophy of the musclefibres. The giant muscle fibres are probably an attempt at compensa-tory hypertrophy. Symptomatology. (a) Landouzy-Dejerine Type.—This type usuallydevelops in early childhood, but I have seen two cases develop in adultlife. The peculiar features are the early atrophy affecting the musclesof the face beginning in the orbicularis oris and extending to the levatormenti, the risorii, and later to the other muscles of the face. The lips ABIOTROPHIC DISEASES 921 become weak and cannot be firmly closed, the mouth is held open withprotruded lips. The upper face muscles usually escape. As the diseaseprogresses the muscles of the neck and shoulder girdle become are no fibrillary tremors of the muscles, no disturbance of sensa-tion, and the reaction of the muscles to mechanical and electric stimuliis gradually lost. The tendon reflexes diminish with the loss of musclepower. Pseudohypertrophic paralysis. The act of rising. This position shows the weakness of the musclesof the neck and the atrophy of the arms. (Starr.)
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Keywords: ., bookcentury1900, bookdecade1900, booksubjectchildren, bookyear190
