A line drawn by a surgeon on a young child awaiting surgery.
The abdomen of an infant with Hurler syndrome; a deficiency in the alpha-L-iduronidase enzyme. Apha-L-iduronidase is responsible for the break down of glycosaminoglycans - a component of connective tissues within the body. With the deficiency of this enzyme, the stores of glycosaminoglycan accumulate. This patient is presented with hepatosplenomegaly
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Photo credit: © Medicshots / Alamy / Afripics
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Keywords: abdomen, alpha--iduronidase, baby, bone, child, deficiency, disease, diseases, enlarged, enzyme, gargoylism, glycosaminoglycans, growth, hepatospleenomegally, hurler, infant, jaundice, large, liver, marking, marrow, mucopolysaccharide, mucopolysaccharidosis, navel, red, spleen, stomach, surgery, syndrome, tr, transplant
