. A treatise on the nervous diseases of children : for physicians and students. lyin life, most of the symptomsbeing fully developed beforethe age of fourteen. In thefamily referred to by EverettSmith, of Boston, the symp-toms of ataxic paraplegiawere observed in the fatherat the age of sixty-six, but it isquestionable whether his wasa typical hereditary ataxy,and it is safer to adhere to the belief that Friedreichs « disease will always appearearly in life. If several mem-bers of one family are affectedthe disease is developed inall at about the same age. Symptoms.—-The symp-tomatology of her
. A treatise on the nervous diseases of children : for physicians and students. lyin life, most of the symptomsbeing fully developed beforethe age of fourteen. In thefamily referred to by EverettSmith, of Boston, the symp-toms of ataxic paraplegiawere observed in the fatherat the age of sixty-six, but it isquestionable whether his wasa typical hereditary ataxy,and it is safer to adhere to the belief that Friedreichs « disease will always appearearly in life. If several mem-bers of one family are affectedthe disease is developed inall at about the same age. Symptoms.—-The symp-tomatology of hereditary at-axy is now as firmly estab-lished as that of almost anyspinal disease. Friedreichdescribed most of the symp-toms in 1861. The Frenchschool, including Charcot,Vulpian, Brissaud, and Ma-rie, have given careful study to this disease. In England,Carpenter, Gowers, Ormerod, and Bury described cases oftrue hereditary ataxy; while in this country the chief con-tributions to this subject have been made by Smith, Ham-mond, Seguin, Dana, Church, Sanger Brown, and Fig. 92.—Same Patient as in Fig. atrophy of the muscles aboutthe shoulder girdles (infra-spinati, su-pra-spinati, rhomboids, and others). 380 THE NERVOUS DISEASES OF CHILDREN. At a very early age children suffering from Friedreichsdisease exhibit peculiarities in walking and standing. Thechild walks with its legs widely apart, in an uncertain, hes-itating fashion, reminding one very strongly of a combinedataxic and cerebellar gait. There are in addition in some pa-tients oscillatory movements of the head, which remind onea little of multiple sclerosis, and a little of such movementsas we sometimes see in cases of senile degeneration. Whenthe patient is asked to stand still, with his feet closely ap-proximated, he soon begins to stagger, as tabic patients do,and as soon as his eyes are closed falls to the ground un-less properly supported. Marie states that Rombergssymptom is ordinarily absent,
Size: 1094px × 2284px
Photo credit: © The Reading Room / Alamy / Afripics
License: Licensed
Model Released: No
Keywords: ., bookcentury1800, bookdecade1890, bookpublishernewyo, bookyear1895
