Diseases of the nervous system : a text-book of neurology and psychiatry . Fig. 163.—Pseudohypertrophicmyopathy. Early stage. (Jen-drassik.) Fig. 164. — Pseudohypertrophic of atrophy. (See 163.) (Jendrassik.) 3. Facio-scapulo-humeral (Landouzy-Dejerine). 4. Atrophic myatonia congenita (Oppenheim). 5. Myatonic atrophica. 6. Distal (Gowers). 7. Mixed and transitional forms. MUSCULAR DYSTROPHIES 331 1. Pseudohyperiroj^hic Type (Duchenne, 1849).—Semmola, in1834, and Costa and Gioja, in 1836, antedated Duchenne in describingthese cases, but pictures of earlier centuries give evidence
Diseases of the nervous system : a text-book of neurology and psychiatry . Fig. 163.—Pseudohypertrophicmyopathy. Early stage. (Jen-drassik.) Fig. 164. — Pseudohypertrophic of atrophy. (See 163.) (Jendrassik.) 3. Facio-scapulo-humeral (Landouzy-Dejerine). 4. Atrophic myatonia congenita (Oppenheim). 5. Myatonic atrophica. 6. Distal (Gowers). 7. Mixed and transitional forms. MUSCULAR DYSTROPHIES 331 1. Pseudohyperiroj^hic Type (Duchenne, 1849).—Semmola, in1834, and Costa and Gioja, in 1836, antedated Duchenne in describingthese cases, but pictures of earlier centuries give evidence of its pres-ence. It is the type most frequently observed. It is more commonin males (3 to 1), and usually begins during childhood. An hereditaryform is very frequent. The parents first notice a certain clumsinessin the gait of the children, then the position of the body is Fig. 165.—Pseudohypertrophic myopathy. Later stage of atrophy. Compare 163, 164. (Jendrassik.) the head being bent forward, and the cervical vertebrae are particularlyprominent. There is an early beginning lumbar lordosis. The patientwaddles, then commences to find it hard to go up stairs—often trips andfalls. On rising from a recumbent position the arms are called in toaid, and the mode of rising is unique. The patient climbs up hislegs as it were with his arms. In the final stages the patient is unableto raise himself at all. 332 LESIONS OF THE SPINAL CORD The shoulder-blades are freely movable and rise with the rise of thearms. Atrophies are apparent. The gait varies somewhat, according to the muscles chiefly is often wabbly, like a pregnant woman; at times it has a high step
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